Products for Research Use Only
RegisterLogin

SGSH Antibody

CAT: 0223-64-012Size: 400 µLDry Ice: NoHazardous: No
Product image 1
1 / 1
CAT#:0223-64-012Size:400 µL
Selected
24/48H Stock Items & 2 to 6 Weeks non Stock Items.
Quick Request Actions
Background
SGSH is one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
NCBI Gene ID
6448
Swiss Prot
P51688
Accession Number
P51688
Host
Rabbit
Reactivity
Human
Immunogen
This SGSH antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 420-449 amino acids from the C-terminal region of human SGSH.
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Neuroscience, Signal Transduction
Purification
This antibody is purified through a protein A column, followed by peptide affinity purification.
Concentration
Batch dependent
Buffer
Supplied in PBS with 0.09% (W/V) sodium azide.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at 4˚ C for three months and -20˚ C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
Calculated Molecular Weight
57 kDa
Fragment
Rabbit Ig
Applications Notes
For WB starting dilution is: 1:4000
Symbol
SGSH
NCBI Official Name
N-sulphoglucosamine sulphohydrolase
NCBI Organism
Homo sapiens
Background Reference 01
Sleat, D.E., et al. Mol. Cell Proteomics 5 (4) :686-701 (2006)
Background Reference 02
Bekri, S., et al. J. Inherit. Metab. Dis. 28 (4) :601-602 (2005)
Background Reference 03
Muschol, N., et al. Hum. Mutat. 23 (6) :559-566 (2004)
Background Reference 04
Zhang, H., et al. Nat. Biotechnol. 21 (6) :660-666 (2003)
Other Product Names
N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulphamidase, SGSH, HSS
Tested Applications
WB
Physical Properties
Liquid

Related Products

CatalogName
64-160WAS Antibody
60-596WAS Antibody
13-349WAS Antibody
62-828Neprilysin Antibody
61-580CAPZB Antibody
55-580HCG_2024410 Antibody
30-580ACPT Antibody
19-580FABP3 Antibody
15-580POMGNT2 Antibody
35-153Cytomegalovirus Antibody

Alternative Products

CatalogName
70R-12598SGSH antibody

Popular Products