LRPPRC antibody

• Background:

  This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR) . The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome.

• Synonyms:

  Leucine-rich PPR motif-containing protein, mitochondrial|130 kDa leucine-rich protein (LRP 130) |GP130|LRPPRC|LRP130

• Gene ID:

  10128

• UniProt:

  P42704

• Host:

  Rabbit

• Reactivity:

  Human, Mouse, Rat

• Immunogen:

  Leucine-rich PPR-motif containing

• Target:

  LRPPRC

• Clonality:

  Polyclonal

• Isotype:

  IgG

• Applications:

  ELISA, WB, IHC

• Field of Research:

  Metabolism

• Purification:

  Immunogen affinity purified

• Dilution:

  WB: 1:1000 - 1:2000; IHC: 1:100 - 1:200

• Purity:

  ≥95% as determined by SDS-PAGE

• Form:

  Liquid

• Molecular Weight:

  140 kDa

• Shipping Conditions:

  4°C with ice bag

• Storage Conditions:

  PBS with 0.02% sodium azide and 50% glycerol pH 7.3, -20°C for 12 months (Avoid repeated freeze / thaw cycles.)

• Tested Applications:

  ELISA, WB, IHC