Products for Research Use Only
RegisterLogin

CLN-2

CAT: 0209-101-M327Size: 50 µgDry Ice: NoHazardous: No
Product image 1
1 / 1
CAT#:0209-101-M327Size:50 µg
Selected
24/48H Stock Items & 2 to 6 Weeks non Stock Items.
Quick Request Actions
Description
Tripeptidyl-peptidase I (TPP1), also known as CLN2, is a lysosomal serine protease detected in all tissues examined, with highest levels shown in heart and placenta. It is an aminopeptidase that cleaves tripeptides from the free N-terminus of polypeptides and may also have endopeptidase activity. Defects in TPP1 are the cause of classical late-infantile neuronal ceroid lipofusionosis, also known as ceroid lipofusionosis neuronal 2 (CLN2), a fatal childhood neurodegenerative disease characterized by progressive visual and mental decline, motor disturbance, epilepsy, and behavioral changes.
Synonyms
TPP1; CLN2; GIG1; LPIC; TPP-1
NCBI Gene ID
1200
UniProt
O14773
Accession Number
NP_000382.3
Accession Number mRNA
NM_000391.3
Chromosomal Location
11p15
Reactivity
Anti-Human
Cross Reactivity
Human
Target Antigen
Recombinant human CLN-2
Clone
(#9V1)
Applications
WB
Purification Method
Protein G chromatography
Assay Protocol
Centrifuge vial prior to opening. Reconstitute the antibody with 500 µl sterile PBS and the final concentration is 200 µg/ml.
Form
Lyophilized
Buffer
PBS
Reconstitution
PBS
Storage Conditions
Lyophilized samples are stable for 2 years from date of receipt when stored at -70°C. Reconstituted antibody can be aliquoted and stored frozen at < -20°C for at least six months without detectable loss of activity.
Host or Source
Mouse
Isotype
IgG2

Related Products

CatalogName
300-050-L500Angiopoietin-2 / Ang-2
300-050Angiopoietin-2 / Ang-2
300-050-L250Angiopoietin-2 / Ang-2
101-M122Angiopoietin-2 / Ang-2
101-M102Angiopoietin-2 / Ang-2
300-049Angiopoietin-2 / Ang-2
300-050-L100Angiopoietin-2 / Ang-2
100-348-L250MIA-2 (Melanoma inhibitory activity 2)
100-348-L500MIA-2 (Melanoma inhibitory activity 2)
100-348-L1000MIA-2 (Melanoma inhibitory activity 2)

Alternative Products

CatalogName
T9901A-600-01CLN-619
GTR18612574-01CLN-619 Antibody
GTR18090316Mouse Monoclonal human CLN-2 Antibody
hAP-0584Mouse Monoclonal anti-human CLN-2
C00522-1mg*5Anti-MICA (CLN-619)
048191MICA (CLN-619) discontinued
GTR18315757MICA Reference Antibody (CLN-619)
F1716-5Anti-MICA Antibody (CLN-619)
216360CLN-2 (Ceroid Lipofuscinosis Neuronal-2, TPP1, Tripeptidyl-peptidase 1)
BIO0394SM-5mgAnti-human MICA (CLN-619 Biosimilar)

Popular Products