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2-Hydroxy-3-methylbutanoic acid

CAT: 1568-C11613-25mgSize: 25 mgDry Ice: NoHazardous: No
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CAT#:1568-C11613-25mgSize:25 mg
Selected
24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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CAS Number
4026-18-0
Synonyms
3-Methyl-2-hydroxybutyric acid, 2-Hydroxyisopentanoic acid, 2-Hydroxyisovaleric acid, alpha-Hydroxyisovaleric acid, 2-Oxyisovaleric acid, 2-Oxyisovalerate
Target
Others
Applications
Others
Smiles
CC (C) C (C (=O) O) O
Molecular Formula
C5H10O3
Additionnal Information
2-Hydroxy-3-methylbutanoic acid (3-Methyl-2-hydroxybutyric acid, 2-Hydroxyisopentanoic acid, 2-Oxyisovaleric acid) is a metabolite found in the urine of patients with phenylketonuria, methylmalonic acidemia, propionic acidemia, 3-ketothiolase deficiency, isovaleric acidemia, 3-methylcrotonylglycemia, 3-hydroxy-3-methylglutaric acidemia, multiple carboxylase deficiency, glutaric aciduria, ornithine transcarbamylase deficiency, glyceroluria, tyrosinemia type I, galactosemia, and maple syrup urine disease.
Storage Conditions
3 years -20°C powder