2-Hydroxy-2-methylbutanoic acid
CAT:
804-HY-W015874-01
Size:
100 mg
For Laboratory Research Only. Not for Clinical or Personal Use.
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- Availability: 24/48H Stock Items & 2 to 6 Weeks non Stock Items.
- Dry Ice Shipment: No


2-Hydroxy-2-methylbutanoic acid
UNSPSC Description:
2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.Target Antigen:
Endogenous MetaboliteType:
Natural ProductsRelated Pathways:
Metabolic Enzyme/ProteaseApplications:
Metabolism-sugar/lipid metabolismField of Research:
Metabolic DiseaseAssay Protocol:
https://www.medchemexpress.com/2-Hydroxy-2-methylbutanoic_acid.htmlPurity:
98.0Solubility:
DMSO : 100 mg/mL (ultrasonic)Smiles:
CCC(C)(O)C(O)=OMolecular Weight:
118.132References & Citations:
[1]Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May;(102):29-71; discussion 95-109.Shipping Conditions:
Room TemperatureStorage Conditions:
-20°C, 3 years; 4°C, 2 years (Powder)Clinical Information:
No Development ReportedCAS Number:
3739-30-8
