2-Hydroxy-2-methylbutanoic acid

CAT:
804-HY-W015874-01
Size:
100 mg

For Laboratory Research Only. Not for Clinical or Personal Use.

  • Availability: 24/48H Stock Items & 2 to 6 Weeks non Stock Items.
  • Dry Ice Shipment: No
2-Hydroxy-2-methylbutanoic acid - image 1

2-Hydroxy-2-methylbutanoic acid

  • UNSPSC Description:

    2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.
  • Target Antigen:

    Endogenous Metabolite
  • Type:

    Natural Products
  • Related Pathways:

    Metabolic Enzyme/Protease
  • Applications:

    Metabolism-sugar/lipid metabolism
  • Field of Research:

    Metabolic Disease
  • Assay Protocol:

    https://www.medchemexpress.com/2-Hydroxy-2-methylbutanoic_acid.html
  • Purity:

    98.0
  • Solubility:

    DMSO : 100 mg/mL (ultrasonic)
  • Smiles:

    CCC(C)(O)C(O)=O
  • Molecular Weight:

    118.132
  • References & Citations:

    [1]Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May;(102):29-71; discussion 95-109.
  • Shipping Conditions:

    Room Temperature
  • Storage Conditions:

    -20°C, 3 years; 4°C, 2 years (Powder)
  • Clinical Information:

    No Development Reported
  • CAS Number:

    3739-30-8