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PEX7 Antibody

CAT: 0223-22-574Size: 100 µLDry Ice: NoHazardous: No
CAT#:0223-22-574Size:100 µL
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Background
This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2) . Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD) .
NCBI Gene ID
5191
Swiss Prot
O00628
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 1-240 of human PEX7 (NP_000279.1) .
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Signal Transduction
Purification
Affinity purification
Positive Control
Mouse heart
Concentration
Batch dependent
Buffer
PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at -20˚ C. Avoid freeze / thaw cycles.
Calculated Molecular Weight
Observed: 36kDa
Fragment
IgG
Applications Notes
WB: 1:500 - 1:2000
Symbol
PEX7
Positive Control 2
Rat liver
NCBI Official Name
Peroxisomal biogenesis factor 7
NCBI Organism
Homo sapiens
Other Product Names
PBD9B, PTS2R, RCDP1, RD, peroxisomal biogenesis factor 7, PTS2 receptor, peroxin-7, peroxisomal PTS2 receptor, peroxisomal targeting signal 2 receptor, peroxisome targeting signal 2 receptor
Tested Applications
WB
Physical Properties
Liquid

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