Products for Research Use Only

2-Methylsuccinic acid

CAT: 0931-T5231-01Size: 1 gDry Ice: NoHazardous: No
Product image 1
1 / 1
CAT#:0931-T5231-01Size:1 g
Selected
24/48H Stock Items & 2 to 6 Weeks non Stock Items.
Quick Request Actions
CAS Number
498-21-5
Target
Endogenous Metabolite
Related Pathways
Metabolism
Purity
0.9931
Bioactivity
2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.
Smiles
C(CC(O)=O)(C(O)=O)C
Molecular Formula
C5H8O4
Molecular Weight
132.11
Shipping Conditions
Ice Packs
Storage Temperature
-20°C