Galactosidase alpha Antibody, Cy7 Conjugated
-
Catalog number
bs-7593R-Cy7
-
Price
Please ask
-
Size
0.1ml
-
-
Long name
Galactosidase alpha Polyclonal Antibody, Cy7 Conjugated
-
Category
Conjugated Primary Antibodies
-
Conjugation
Cy7
-
Host Organism
Rabbit (Oryctolagus cuniculus)
-
Target Antigen
Galactosidase alpha
-
Specificity
This is a highly specific antibody against Galactosidase alpha.
-
Modification
Unmodified
-
Modification site
None
-
Clonality
Polyclonal
-
Clone
Polyclonal antibody
-
Concentration
1ug per 1ul
-
Immunogen_range
127-148/429
-
Subcellular location
Lysosome
-
Source
KLH conjugated synthetic peptide derived from human Galactosidase alpha
-
Gene ID number
2717
-
Swiss Prot
P06280
-
Tested applications
IF(IHC-P)
-
Recommended dilutions
IF(IHC-P)(1:50-200)
-
Crossreactivity
Human, Mouse, Rat
-
Crossreactive species details
Due to limited amount of testing and knowledge, not every possible cross-reactivity is known.
-
Antigen background
Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.
-
Purification method
This antibody was purified via Protein A.
-
Storage conditions
Keep the antibody in an aqueous buffered solution containing 1% BSA, 50% glycerol and 0.09% sodium azide. Store refrigerated at 2 to 8 degrees Celcius for up to 1 year.
-
Excitation Emission
743nm/767nm
-
Synonyms
GALA; Alpha-galactosidase A; Alpha-D-galactosidase A; Alpha-D-galactoside galactohydrolase; Melibiase; GLA
-
Description
The Anti-Galactosidase alpha is a α- or alpha protein sometimes glycoprotein present in blood.
-
Properties
If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24°C for long term storage and for short term at + 5°C.
-
Conjugated
These antibodies are excite for emission at 650 nm and detected at a 676 nm wavelengths.
-
Additional conjugation
Cy7
-
French translation
anticorps
-
Gene target
-
Short name
Anti-Galactosidase alpha
-
Technique
Antibody, antibodies against human proteins, antibodies for, antibody Conjugates
-
Isotype
Immunoglobulin G (IgG)
-
Label
Cy7
-
Alternative name
Anti-Galactosidase alpha PAb Cy7
-
Alternative technique
antibodies
-
MeSH Data
-
Name
-
Concept
Scope note:
Identification of proteins or peptides that have been electrophoretically separated by blot transferring from the electrophoresis gel to strips of nitrocellulose paper, followed by labeling with antibody probes.
-
Tree numbers
- E05.196.401.143
- E05.301.300.096
- E05.478.566.320.200
- E05.601.262
- E05.601.470.320.200
-
Qualifiers
ethics, trends, veterinary, history, classification, economics, instrumentation, methods, standards, statistics & numerical data
Product images
Similar products