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FKRP Antibody

CAT: 0399-CSB-PA060135-01Size: 50 µgDry Ice: NoHazardous: No
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CAT#:0399-CSB-PA060135-01Size:50 µg
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Gene Aliases
Fkrp antibody; FKRP_HUMAN antibody; FLJ12576 antibody; Fukutin related protein antibody; Fukutin-related protein antibody; LGMD2I antibody; MDC1C antibody; MGC2991 antibody
UniProt
Q9H9S5
Host
Rabbit
Antigen Species
Human
Reactivity
Human, Mouse, Rat
Target Antigen
Synthesized peptide derived from the N-terminal region of Human FKRP.
Target
FKRP
Clonality
Polyclonal
Conjugation
Non-conjugated
Field of Research
Signal Transduction
Purification Method
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Form
Liquid
Buffer
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Storage Conditions
Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Antibody Type
Polyclonal Antibody
Tested Applications
WB, IF, ELISA; WB:1:500-1:2000, IF:1:200-1:1000, ELISA:1:20000
Isotype
IgG

UniProtKB · Q9H9S5

Ribitol 5-phosphate transferase FKRP

FKRP_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
Q9H9S5
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
FKRP
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
—
EC number
2.7.8.-
Processing
—
Secondary accessions
A8K5G7
Protein keywords

Technical term

3D-structureProteomics identificationReference proteome

Disease

CardiomyopathyCongenital muscular dystrophyDisease variantDystroglycanopathyLimb-girdle muscular dystrophyLissencephaly

Cellular component

Cell membraneCytoplasmEndoplasmic reticulumGolgi apparatusMembraneSecreted

PTM

Disulfide bondGlycoprotein

Ligand

MagnesiumMetal-bindingZinc

Domain

Signal-anchorTransmembraneTransmembrane helix

Molecular function

Transferase

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