Products for Research Use Only

GBA Mouse mAb

CAT: 0013-GTR18322628-02Size: 100 µLDry Ice: NoHazardous: No
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CAT#:0013-GTR18322628-02Size:100 µL
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Description
GBA Mouse mAb
Product Name Alternative
Alglucerase; betaGC; GBA1; GCase; GCB; GLUC; Glucosylceramidase; Imiglucerase
UniProt
P04062
Reactivity
Human
Immunogen
Human recombinant protein fragment of human GBA (NP_000148) produced in E.coli.
Clonality
Monoclonal
Clone
BBP393
Conjugation
Unconjugated
Field of Research
Metabolism Research
Purification
Affinity Chromatography
Concentration
0.5-1.0 mg/ml
Dilution
IHC: 1/50-1/100
Form
Liquid
Storage Conditions
Maintain refrigerated at 2-8°C for up to 2 weeks. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.
Notes
For research use only.
Tested Applications
IHC-P
Preservative
PBS (PH 7.3) containing 1% rAlbumin, 50% glycerol and 0.02% sodium azide.
Isotype
IgG2a

UniProtKB · P04062

Lysosomal acid glucosylceramidase

GBA1_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
P04062
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
GBA1
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
Lysosomal acid GCase
EC number
3.2.1.45
Processing
Precursor
Secondary accessions
A8K796, B7Z5G2, B7Z6S1, J3KQG4, J3KQK9, Q16545, Q4VX22, Q6I9R6, Q9UMJ8
Protein keywords

Technical term

3D-structureDirect protein sequencingPharmaceuticalProteomics identificationReference proteome

Coding sequence diversity

Alternative initiationAlternative splicing

Biological process

Cholesterol metabolismLipid metabolismSphingolipid metabolismSteroid metabolismSterol metabolism

Disease

Disease variantGaucher diseaseIchthyosisNeurodegenerationParkinson diseaseParkinsonism

PTM

Disulfide bondGlycoprotein

Molecular function

GlycosidaseGlycosyltransferaseHydrolaseTransferase

Cellular component

LysosomeMembrane

Domain

Signal

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