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Cleaved-LMNA (D230) Antibody

CAT: 0399-CSB-PA000047-01Size: 50 µgDry Ice: NoHazardous: No
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CAT#:0399-CSB-PA000047-01Size:50 µg
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Gene Aliases
70 kDa lamin antibody; Cardiomyopathy dilated 1A (autosomal dominant) antibody; CDCD1 antibody; CDDC antibody; CMD1A antibody; CMT2B1 antibody; EMD2 antibody; FPL antibody; FPLD antibody; FPLD2 antibody; HGPS antibody; IDC antibody; Lamin A antibody; Lamin A/C antibody; Lamin A/C like 1 antibody; Lamin antibody; Lamin C antibody; lamin-a antibody; Lamin-A/C antibody; LDP1 antibody; LFP antibody; LGMD1B antibody; Limb girdle muscular dystrophy 1B (autosomal dominant) antibody; LMN 1 antibody; LMN A antibody; LMN C antibody; LMN1 antibody; LMNA antibody; LMNA_HUMAN antibody; LMNC antibody; LMNL1 antibody; Prelamin A/C antibody; PRO1 antibody; Renal carcinoma antigen NY REN 32 antibody; Renal carcinoma antigen NY-REN-32 antibody; Renal carcinoma antigen NYREN32 antibody
UniProt
P02545
Host
Rabbit
Antigen Species
Human
Reactivity
Human, Mouse, Rat
Target Antigen
Synthesized peptide derived from the Internal region of Human Lamin A.
Target
LMNA
Clonality
Polyclonal
Conjugation
Non-conjugated
Field of Research
Cell Biology
Purification Method
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
Form
Liquid
Buffer
Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
Storage Conditions
Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
Antibody Type
Polyclonal Antibody
Tested Applications
WB, IHC, ELISA; WB:1:500-1:2000, IHC:1:100-1:300, ELISA:1:10000
Isotype
IgG

UniProtKB · P02545

Prelamin-A/C

LMNA_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
P02545
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
LMNA
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
—
EC number
—
Processing
Precursor
Secondary accessions
B4DI32, D3DVB0, D6RAQ3, E7EUI9, P02546, Q5I6Y4, Q5I6Y6, Q5TCJ2, Q5TCJ3, Q6UYC3, Q969I8, Q96JA2
Protein keywords

Technical term

3D-structureDirect protein sequencingProteomics identificationReference proteome

PTM

AcetylationGlycoproteinIsopeptide bondLipoproteinMethylationPhosphoproteinPrenylationUbl conjugation

Coding sequence diversity

Alternative splicing

Disease

CardiomyopathyCharcot-Marie-Tooth diseaseCongenital muscular dystrophyDisease variantEmery-Dreifuss muscular dystrophyLimb-girdle muscular dystrophyNeurodegenerationNeuropathy

Domain

Coiled coil

Cellular component

Intermediate filamentNucleus