Products for Research Use Only

FKRP Rabbit Polyclonal Antibody

CAT: 0013-GTR18233133-01Size: 50 μLDry Ice: NoHazardous: No
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CAT#:0013-GTR18233133-01Size:50 μL
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Description
FKRP Rabbit Polyclonal Antibody
UniProt
Q9H9S5
Reactivity
Human, Mouse, Rat
Clonality
Polyclonal
Conjugation
Unconjugated
Field of Research
Cell Biology
Storage Conditions
Maintain refrigerated at 2-8°C for up to 2 weeks. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.
Notes
For research use only.
Tested Applications
IHC, WB
Host or Source
Rabbit

UniProtKB · Q9H9S5

Ribitol 5-phosphate transferase FKRP

FKRP_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
Q9H9S5
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
FKRP
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
—
EC number
2.7.8.-
Processing
—
Secondary accessions
A8K5G7
Protein keywords

Technical term

3D-structureProteomics identificationReference proteome

Disease

CardiomyopathyCongenital muscular dystrophyDisease variantDystroglycanopathyLimb-girdle muscular dystrophyLissencephaly

Cellular component

Cell membraneCytoplasmEndoplasmic reticulumGolgi apparatusMembraneSecreted

PTM

Disulfide bondGlycoprotein

Ligand

MagnesiumMetal-bindingZinc

Domain

Signal-anchorTransmembraneTransmembrane helix

Molecular function

Transferase