Products for Research Use Only

Frataxin Antibody

CAT: 0013-GTR18179434Size: 100 µgDry Ice: NoHazardous: No
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CAT#:0013-GTR18179434Size:100 µg
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Description
Mouse monoclonal antibody to Frataxin (FXN)
UniProt
Q16595
Reactivity
Human
Immunogen
Full length human recombinant protein of human FXN (NP_000135) produced in HEK293T cell.
Target
Frataxin
Clonality
Monoclonal
Clone
BQVK5H5
Conjugation
Unconjugated
Dilution
WB 1:500
Molecular Weight
18.8 kDa
Storage Conditions
Maintain refrigerated at 2-8°C for up to 2 weeks. For long term storage store at -20°C in small aliquots to prevent freeze-thaw cycles.
Notes
For research use only.
Applications Notes
For reconstitution, we recommend adding 100uL distilled water to a final antibody concentration of about 1 mg/mL. To use this carrier-free antibody for conjugation experiment, we strongly recommend performing another round of desalting process.
Tested Applications
WB
NCBI Accession Number
NM_000144
Host or Source
Mouse
Isotype
IgG1

UniProtKB · Q16595

Frataxin, mitochondrial

FRDA_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
Q16595
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
FXN
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
—
EC number
1.16.3.1
Processing
Precursor
Secondary accessions
A8MXJ6, C9JJ89, O15545, O95656, Q15294, Q5VZ01
Protein keywords

Technical term

3D-structureDirect protein sequencingProteomics identificationReference proteome

Coding sequence diversity

Alternative splicingTriplet repeat expansion

Cellular component

CytoplasmMitochondrion

Disease

Disease variant

Biological process

Heme biosynthesisIon transportIron storageIron transportTransport

Ligand

IronMetal-binding

Molecular function

Oxidoreductase

Domain

Transit peptide