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FH Polyclonal Antibody

CAT: 0965-JOT-AP09147-01Size: 20 µLDry Ice: NoHazardous: No
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CAT#:0965-JOT-AP09147-01Size:20 µL
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Background
The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy.
CAS Number
9007-83-4
Synonyms
Fumarate hydratase, mitochondrial; Fumarate hydratase, mitochondrial; Fumarase; EC 4.2.1.2
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant Protein of Fumarate hydratase, mitochondrial
Clonality
Polyclonal
Applications
WB
Stability
-20°C for 1 year
Antibody Type
Primary antibody
Isotype
IgG