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ECHA Rabbit Polyclonal Antibody

CAT: 0965-JOT-AP09422-01Size: 20 µLDry Ice: NoHazardous: No
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CAT#:0965-JOT-AP09422-01Size:20 µL
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Background
This gene encodes the alpha subunit of the mitochondrial trifunctional protein| which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits| with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
CAS Number
9007-83-4
Synonyms
ECHA; Trifunctional enzyme subunit alpha; mitochondrial; 78 kDa gastrin-binding protein; TP-alpha [Includes: Long-chain enoyl-CoA hydratase; EC 4.2.1.17; Long chain 3-hydroxyacyl-CoA dehydrogenase; EC 1.1.1.211;
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Synthesized peptide derived from human ECHA
Clonality
Polyclonal
Applications
WB
Stability
-20°C for 1 year
Concentration
1 mg/ml
Antibody Type
Primary antibody
Isotype
IgG