Glutarylcarnitine
CAT:
804-HY-113005-01
Size:
10 mg
Price:
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- Availability: 24/48H Stock Items & 2 to 6 Weeks non Stock Items.
- Dry Ice Shipment: No

Glutarylcarnitine
- CAS Number: 102636-82-8
- UNSPSC Description: Glutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
- Target Antigen: Endogenous Metabolite
- Type: Natural Products
- Related Pathways: Metabolic Enzyme/Protease
- Applications: Metabolism-protein/nucleotide metabolism
- Field of Research: Metabolic Disease
- Assay Protocol: https://www.medchemexpress.com/Glutarylcarnitine.html
- Purity: 95.03
- Solubility: DMSO : 2 mg/mL (ultrasonic;warming;heat to 60°C)|Ethanol : 100 mg/mL (ultrasonic)
- Smiles: C[N+](C)(C)C[C@H](OC(CCCC(O)=O)=O)CC([O-])=O
- Molecular Weight: 275.30
- References & Citations: [1]Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27(6):789-90.|[2]S Tortorelli, et al. The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I. Mol Genet Metab. 2005 Feb;84(2):137-43.
- Shipping Conditions: Room Temperature
- Storage Conditions: -20°C, 3 years; 4°C, 2 years (Powder)
- Clinical Information: No Development Reported