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Recombinant GBA Antibody

CAT: 0667-RC-16721-01Size: 50 μLDry Ice: NoHazardous: No
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CAT#:0667-RC-16721-01Size:50 μL
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Product Name Alternative
Lysosomal acid glucosylceramidase, Lysosomal acid GCase, Acid beta-glucosidase, Alglucerase, Beta-glucocerebrosidase, Beta-GC, Beta-glucosylceramidase 1, Cholesterol glucosyltransferase, SGTase, Cholesteryl-beta-glucosidase, D-glucosyl-N-acylsphingosine glucohydrolase, Glucosylceramidase beta 1, Imiglucerase, Lysosomal cholesterol glycosyltransferase, Lysosomal galactosylceramidase, Lysosomal glycosylceramidase
Gene Name
GBA
Gene ID
2629
UniProt
P04062
Antigen Species
Human
Reactivity
Human, Rat
Cross Reactivity
Not tested
Immunogen
A synthesized peptide derived from human GBA
Partner Proteins
Lysosomal acid glucosylceramidase; Lysosomal acid GCase; Acid beta-glucosidase; Alglucerase; Beta-glucocerebrosidase; Beta-GC; Beta-glucosylceramidase 1; Cholesterol glucosyltransferase; SGTase; Cholesteryl-beta-glucosidase; D-glucosyl-N-acylsphingosine glucohydrolase; Glucosylceramidase beta 1; Imiglucerase; Lysosomal cholesterol glycosyltransferase; Lysosomal galactosylceramidase; Lysosomal glycosylceramidase
Clone
K01_4R47
Conjugation
Unconjugated
Applications
WB
Validation
WB
Purity
≥85%
Storage Temperature
Avoid repeated freeze-thaw cycles. Upon receipt, * 1 month when stored at 2 to 8 °C * 12 months when aliquoted and stored at -20 °C or lower
Recombinant Antibody
Yes
WB Dilution
1:500~1:1000
Formulation
10mM PBS, pH 7.4, 150mM sodium chloride, 0.05% BSA, 0.02% sodium azide and 50% glycerol.
Antibody Type
Monoclonal
Gene Name Synonym
GBA; GC; GLUC
Target Alternative Name
GBA
Panel Description
Neurodegenerative Diseases Marker, Neuroscience Biomarkers
Host or Source
Rabbit
Protein Name
Glucosylceramidase beta 1
WB Description
Succeed
Shipping Temperature
Shipped at ambient temperature or with ice packs.
Isotype
IgG

UniProtKB · P04062

Lysosomal acid glucosylceramidase

GBA1_HUMAN · Homo sapiens

View on UniProt ↗
Primary accession
P04062
Review status
UniProtKB reviewed (Swiss-Prot)
Gene
GBA1
Protein existence
1: Evidence at protein level
Organism
Homo sapiens (Human)
Taxonomy ID
9606
Alternative names
Lysosomal acid GCase
EC number
3.2.1.45
Processing
Precursor
Secondary accessions
A8K796, B7Z5G2, B7Z6S1, J3KQG4, J3KQK9, Q16545, Q4VX22, Q6I9R6, Q9UMJ8
Protein keywords

Technical term

3D-structureDirect protein sequencingPharmaceuticalProteomics identificationReference proteome

Coding sequence diversity

Alternative initiationAlternative splicing

Biological process

Cholesterol metabolismLipid metabolismSphingolipid metabolismSteroid metabolismSterol metabolism

Disease

Disease variantGaucher diseaseIchthyosisNeurodegenerationParkinson diseaseParkinsonism

PTM

Disulfide bondGlycoprotein

Molecular function

GlycosidaseGlycosyltransferaseHydrolaseTransferase

Cellular component

LysosomeMembrane

Domain

Signal