HIBCH Mouse Monoclonal Antibody [Clone ID: LBI3B10]

• Background:

  This gene encodes the enzyme responsible for hydrolysis of both HIBYL-CoA and beta-hydroxypropionyl-CoA. Mutations in this gene have been associated with 3-hyroxyisobutyryl-CoA hydrolase deficiency. Alternative splicing results in multiple transcript variants.

• Synonyms:

  HIBYLCOAH

• Gene Name:

  3-hydroxyisobutyryl-CoA hydrolase

• Gene ID:

  26275

• UniProt:

  Q6NVY1

• Conjugation:

  Unconjugated

• Related Pathways:

  Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

• Field of Research:

  Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

• Concentration:

  0.6 mg/ml

• Dilution:

  WB 1:2000, IF 1:100, FLOW 1:100

• Form:

  PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

• Buffer:

  PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

• Storage Conditions:

  Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

• Symbol:

  HIBCH

• Overview:

  Anti-HIBCH mouse monoclonal antibody, clone LBI3B10

• Gene ID URL:

  https://www.ncbi.nlm.nih.gov/gene/?term=26275

• Uniprot URL:

  https://www.uniprot.org/uniprot/Q6NVY1