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2,4-Dihydroxybutanoic acid

CAT: 0013-GTR19240279-01Size: 50 mgDry Ice: NoHazardous: No
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CAT#:0013-GTR19240279-01Size:50 mg
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Description
2,4-Dihydroxybutanoic acid is a metabolite normally absent in human urine but significantly elevated in succinic semialdehyde dehydrogenase deficiency. It serves as a key biomarker for researching this neurometabolic disorder in both clinical and experimental settings, including in vitro enzyme studies and in vivo metabolic profiling.
CAS Number
1518-62-3
Field of Research
Metabolism Research
Smiles
O=C (O) C (O) CCO
Molecular Formula
C4H8O4
Molecular Weight
120.10
Storage Conditions
-20°C
Notes
For research use only.