Products for Research Use Only

3-Hydroxyisovalerylcarnitine

CAT: 0013-GTR19233748-01Size: 50 mgDry Ice: NoHazardous: No
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CAT#:0013-GTR19233748-01Size:50 mg
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24/48H Stock Items & 2 to 6 Weeks non Stock Items.
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Description
3-Hydroxyisovalerylcarnitine is a biomarker for biotin deficiency, as its elevated plasma levels indicate impaired leucine catabolism due to reduced 3-methylcrotonyl-CoA carboxylase activity. This small molecule is utilized in research applications involving metabolic disorder studies, biomarker validation, and in vitro diagnostic assay development.
CAS Number
99159-87-2
Field of Research
Metabolism Research
Smiles
O ([C@@H] (C[N+] (C) (C) C) CC ([O-]) =O) C (CC (C) (C) O) =O
Molecular Formula
C12H23NO5
Molecular Weight
261.32
Storage Conditions
-20°C
Notes
For research use only.